Cemil Yıldırım Türk1, Ahmet Güney2, Mithat Öner2, Mehmet Halıcı2

02Orthopedics and Traumatology, Medicine Faculty of Erciyes University, Kayseri, Turkey
Orthopedics and Traumatology,
1Department of Orthopedics and Traumatology, Division of Hand Surgery

Keywords: Hand; lymphangioma; macrodactyly; Proteus syndrome; syndactyly.


Proteus syndrome is a complex disorder characterized by a wide variety of deformities including macrodactyly. In the present report, we present a case with complex macrosyndactyly in his hand. The patient was surgically treated. However, he admitted with lymphangiomas on his body during the follow- up period, leading to the diagnosis of Proteus syndrome. This article discusses the differential diagnosis of Proteus syndrome and the treatment methods used for macrodactyly along with the presentation of the case.