Güven Ozan Kaplan1, Fethiye Damla Menku Özdemir1, Diclehan Orhan2, Ali Emre Aksu1, Figen Özgür1

1Department of Plastic, Reconstructive and Aesthetic Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey
2Department of Pathology, Hacettepe University Faculty of Medicine, Ankara, Turkey

Keywords: Dabska tumor, pathology, skin tumor, soft tissue neoplasm

Abstract

Papillary intralymphatic angioendothelioma (PILA), an intralymphatic lesion of vascular ducts, is an extremely rare tumor. It is generally encountered as an unexpected pathology following excision of a vascular skin lesion. Re-excision is the commonly preferred treatment option once the pathological diagnosis is established. In this article, we present a 12-year-old male patient with a PILA treated with re-excision, skin grafting, and sentinel lymph node biopsy. The patient was symptom-free at annual follow-up. A sentinel lymph node biopsy during re-excision might be a good option in the surgical management of PILA. Frequent examination of lymph nodes and skin lesion also might be beneficial during the follow-ups.

Citation: Kaplan GO, Menku Özdemir FD, Orhan D, Aksu AE, Özgür F. Papillary intralymphatic angioendothelioma: An extremely rare tumor. Jt Dis Relat Surg 2021;32(1):245-248.

Conflict of Interest

The authors declared no conflicts of interest with respect to the authorship and/or publication of this article.

Financial Disclosure

The authors received no financial support for the research and/or authorship of this article.